Department of Neurology, Washington University School of Medicine, St. Louis, MO 63110, USA.
Sci Transl Med. 2011 Jun 29;3(89):89ra57. doi: 10.1126/scitranslmed.3002156.
The apolipoprotein E (APOE) ε4 allele is the strongest genetic risk factor for late-onset, sporadic Alzheimer's disease (AD). The APOE ε4 allele markedly increases AD risk and decreases age of onset, likely through its strong effect on the accumulation of amyloid-β (Aβ) peptide. In contrast, the APOE ε2 allele appears to decrease AD risk. Most rare, early-onset forms of familial AD are caused by autosomal dominant mutations that often lead to overproduction of Aβ(42) peptide. However, the mechanism by which APOE alleles differentially modulate Aβ accumulation in sporadic, late-onset AD is less clear. In a cohort of cognitively normal individuals, we report that reliable molecular and neuroimaging biomarkers of cerebral Aβ deposition vary in an apoE isoform-dependent manner. We hypothesized that human apoE isoforms differentially affect Aβ clearance or synthesis in vivo, resulting in an apoE isoform-dependent pattern of Aβ accumulation later in life. Performing in vivo microdialysis in a mouse model of Aβ-amyloidosis expressing human apoE isoforms (PDAPP/TRE), we find that the concentration and clearance of soluble Aβ in the brain interstitial fluid depends on the isoform of apoE expressed. This pattern parallels the extent of Aβ deposition observed in aged PDAPP/TRE mice. ApoE isoform-dependent differences in soluble Aβ metabolism are observed not only in aged but also in young PDAPP/TRE mice well before the onset of Aβ deposition in amyloid plaques in the brain. Additionally, amyloidogenic processing of amyloid precursor protein and Aβ synthesis, as assessed by in vivo stable isotopic labeling kinetics, do not vary according to apoE isoform in young PDAPP/TRE mice. Our results suggest that APOE alleles contribute to AD risk by differentially regulating clearance of Aβ from the brain, suggesting that Aβ clearance pathways may be useful therapeutic targets for AD prevention.
载脂蛋白 E (APOE) ε4 等位基因是晚发性、散发性阿尔茨海默病 (AD) 的最强遗传风险因素。APOE ε4 等位基因显著增加 AD 风险并降低发病年龄,这可能是通过其对淀粉样蛋白-β (Aβ) 肽的积累产生强烈影响所致。相比之下,APOE ε2 等位基因似乎降低 AD 风险。大多数早发性家族性 AD 是由常染色体显性突变引起的,这些突变通常导致 Aβ(42)肽的过度产生。然而,APOE 等位基因如何在散发性、晚发性 AD 中差异调节 Aβ 积累的机制尚不清楚。在一组认知正常的个体中,我们报告说,大脑 Aβ 沉积的可靠分子和神经影像学生物标志物以 apoE 同工型依赖的方式变化。我们假设人类 apoE 同工型在体内以不同的方式影响 Aβ 的清除或合成,从而导致生命后期 apoE 同工型依赖的 Aβ 积累模式。在表达人 apoE 同工型的 Aβ-淀粉样蛋白淀粉样变性小鼠模型中进行体内微透析,我们发现脑间质液中可溶性 Aβ 的浓度和清除取决于表达的 apoE 同工型。这种模式与老年 PDAPP/TRE 小鼠中观察到的 Aβ 沉积程度相平行。不仅在老年 PDAPP/TRE 小鼠中,而且在大脑淀粉样斑块中 Aβ 沉积之前的年轻 PDAPP/TRE 小鼠中,也观察到 apoE 同工型依赖性差异的可溶性 Aβ 代谢。此外,通过体内稳定同位素标记动力学评估,年轻 PDAPP/TRE 小鼠中 apoE 同工型不影响淀粉样前体蛋白的淀粉样生成处理和 Aβ 合成。我们的研究结果表明,APOE 等位基因通过差异调节 Aβ 从大脑中的清除来增加 AD 风险,这表明 Aβ 清除途径可能是 AD 预防的有用治疗靶点。