Umbetalina N S, Turgunov E M, Turgunova L G, Baesheva T A, Bacheva I V
Ter Arkh. 2014;86(12):78-80. doi: 10.17116/terarkh2014861278-80.
The Rapunzel syndrome is a rare complication of gastric trichobezoar, which may be long insidious. Systemic hair eating gradually leads to bezoar growth, gastritis, gastric mucosal ulcerations, and evacuatory disorders. The Rapunzel syndrome may cause acute and chronic bowel obstruction, peritonitis, pancreatitis, appendicitis, anemia, hypoalbuminemia, and allergic manifestations. Neither proteinuria nor nephrotic syndrome is depicted in any of the 38 Rapunzel syndrome cases described in the literature. The authors present the first case of gastric trichobezoar extending to the small bowel (its total length was 118 cm), which gave rise to chronic recurrent partial bowel obstruction, causing intoxication nephrotic syndrome in a 20-year-old women with trichotillomania. The nephrotic syndrome became a reason for her admission to a nephrology department and had specific features: it was unaccompanied by hypercholesterolemia, it rapidly regressed and completely disappeared after surgical removal of the trichobezoar weighing 1980 g.
长发公主综合征是胃毛石症的一种罕见并发症,可能长期隐匿。系统性食毛逐渐导致毛石生长、胃炎、胃黏膜溃疡和排空障碍。长发公主综合征可引起急慢性肠梗阻、腹膜炎、胰腺炎、阑尾炎、贫血、低白蛋白血症和过敏表现。文献中描述的38例长发公主综合征病例均未提及蛋白尿或肾病综合征。作者报告了首例胃毛石延伸至小肠(全长118厘米)的病例,该病例导致一名患有拔毛癖的20岁女性出现慢性复发性部分肠梗阻,并引发中毒性肾病综合征。肾病综合征是她入住肾病科的原因,且具有特殊特征:不伴有高胆固醇血症,在手术切除重达1980克的毛石后迅速消退并完全消失。