Inositide Laboratory, Babraham Institute, Cambridge, United Kingdom.
Blood. 2010 Dec 23;116(26):6027-36. doi: 10.1182/blood-2010-08-300889. Epub 2010 Sep 22.
The neutrophil nicotinamide adenine dinucleotide phosphate-oxidase is a multisubunit enzyme (comprising gp91(phox), p22(phox), p67(phox), p40(phox), p47(phox), and Rac) that plays a vital role in microbial killing. The recent discovery of a chronic granulomatous disease patient who expresses a mutant p40(phox) subunit, together with the development of mouse models of p40(phox) function, indicate phosphatidylinositol 3-phosphate binding to the PX domain of p40(phox) is an important signal for oxidase activation. However, the presence of other conserved residues and domains in p40(phox) suggest further regulatory roles for this protein. To test this, we introduced wild-type and mutated versions of p40(phox) into fully differentiated mouse neutrophils by retroviral transduction of p40(phox)(-/-) bone marrow progenitors and repopulation of the bone marrow compartment in radiation chimaeras. Phosphorylation of p40(phox) on threonine 154, but not serine 315, was required for full oxidase activation in response to formylated bacterial peptide fMLP, serum-opsonized S aureus, and immunoglobulin-opsonized sheep red blood cells. A functional SH3 domain was not required for oxidase activation, and deletion of the entire domain resulted in enhanced oxidase responses. Phosphorylation of threonine 154 in response to S aureus was mediated by protein kinase Cδ and was required for full translocation of p47(phox) to phagosomes. These results define an important new element in the physiological activation of the oxidase.
中性粒细胞烟酰胺腺嘌呤二核苷酸磷酸氧化酶是一种多亚基酶(包含 gp91(phox)、p22(phox)、p67(phox)、p40(phox)、p47(phox)和 Rac),在微生物杀伤中起着至关重要的作用。最近发现了一位表达突变 p40(phox)亚基的慢性肉芽肿病患者,以及 p40(phox)功能的小鼠模型的发展,表明磷脂酰肌醇 3-磷酸与 p40(phox)的 PX 结构域结合是氧化酶激活的重要信号。然而,p40(phox)中存在其他保守残基和结构域表明该蛋白具有进一步的调节作用。为了验证这一点,我们通过逆转录病毒转导 p40(phox)(-/-)骨髓祖细胞并在辐射嵌合体中重新填充骨髓腔,将野生型和突变型 p40(phox)引入完全分化的小鼠中性粒细胞中。在对细菌肽 fMLP、血清调理的金黄色葡萄球菌和免疫球蛋白调理的绵羊红细胞的反应中,p40(phox)上丝氨酸 315 而不是苏氨酸 154 的磷酸化对于完全氧化酶激活是必需的。功能性 SH3 结构域对于氧化酶激活不是必需的,并且整个结构域的缺失导致氧化酶反应增强。金黄色葡萄球菌引起的苏氨酸 154 的磷酸化由蛋白激酶 Cδ介导,并且对于 p47(phox)向吞噬体的完全易位是必需的。这些结果定义了氧化酶生理激活中的一个重要新要素。