Department of Medicine, Duke University Medical Center, Durham, NC 27710, USA.
Leukemia. 2011 Sep;25(9):1459-66. doi: 10.1038/leu.2011.117. Epub 2011 May 27.
Monoclonal B-cell lymphocytosis (MBL) is a hematologic condition wherein small B-cell clones can be detected in the blood of asymptomatic individuals. Most MBL have an immunophenotype similar to chronic lymphocytic leukemia (CLL), and 'CLL-like' MBL is a precursor to CLL. We used flow cytometry to identify MBL from unaffected members of CLL kindreds. We identified 101 MBL cases from 622 study subjects; of these, 82 individuals with MBL were further characterized. In all, 91 unique MBL clones were detected: 73 CLL-like MBL (CD5(+)CD20(dim)sIg(dim)), 11 atypical MBL (CD5(+)CD20(+)sIg(+)) and 7 CD5(neg) MBL (CD5(neg)CD20(+)sIg(neg)). Extended immunophenotypic characterization of these MBL subtypes was performed, and significant differences in cell surface expression of CD23, CD49d, CD79b and FMC-7 were observed among the groups. Markers of risk in CLL such as CD38, ZAP70 and CD49d were infrequently expressed in CLL-like MBL, but were expressed in the majority of atypical MBL. Interphase cytogenetics was performed in 35 MBL cases, and del 13q14 was most common (22/30 CLL-like MBL cases). Gene expression analysis using oligonucleotide arrays was performed on seven CLL-like MBL, and showed activation of B-cell receptor associated pathways. Our findings underscore the diversity of MBL subtypes and further clarify the relationship between MBL and other lymphoproliferative disorders.
单克隆 B 细胞淋巴增生症 (MBL) 是一种血液学病症,其中无症状个体的血液中可检测到小 B 细胞克隆。大多数 MBL 的免疫表型与慢性淋巴细胞白血病 (CLL) 相似,而“CLL 样”MBL 是 CLL 的前体。我们使用流式细胞术从 CLL 家族中未受影响的成员中识别 MBL。我们从 622 名研究对象中确定了 101 例 MBL 病例;其中,82 例 MBL 患者进一步进行了特征描述。总共检测到 91 个独特的 MBL 克隆:73 例 CLL 样 MBL(CD5(+)CD20(dim)sIg(dim)),11 例非典型 MBL(CD5(+)CD20(+)sIg(+))和 7 例 CD5(neg) MBL(CD5(neg)CD20(+)sIg(neg))。对这些 MBL 亚型进行了扩展的免疫表型特征描述,观察到各组之间 CD23、CD49d、CD79b 和 FMC-7 细胞表面表达存在显著差异。CLL 中的风险标志物如 CD38、ZAP70 和 CD49d 在 CLL 样 MBL 中很少表达,但在大多数非典型 MBL 中表达。对 35 例 MBL 进行了间期细胞遗传学检查,最常见的是 del 13q14(22/30 例 CLL 样 MBL 病例)。对 7 例 CLL 样 MBL 进行了寡核苷酸微阵列基因表达分析,显示 B 细胞受体相关途径的激活。我们的研究结果强调了 MBL 亚型的多样性,并进一步阐明了 MBL 与其他淋巴增生性疾病之间的关系。