Departments of Medicine and Molecular Pharmacology, Albert Einstein College of Medicine, Bronx, New York 10461, USA.
Mol Aspects Med. 2013 Apr-Jun;34(2-3):373-85. doi: 10.1016/j.mam.2012.07.006.
The reduced folate carrier (RFC, SLC19A1), thiamine transporter-1 (ThTr1, SLC19A2) and thiamine transporter-2 (ThTr2, SLC19A3) evolved from the same family of solute carriers. SLC19A1 transports folates but not thiamine. SLC19A2 and SLC19A3 transport thiamine but not folates. SLC19A1 and SLC19A2 deliver their substrates to systemic tissues; SLC19A3 mediates intestinal thiamine absorption. The proton-coupled folate transporter (PCFT, SLC46A1) is the mechanism by which folates are absorbed across the apical-brush-border membrane of the proximal small intestine. Two folate receptors (FOLR1 and FOLR2) mediate folate transport across epithelia by an endocytic process. Folate transporters are routes of delivery of drugs for the treatment of cancer and inflammatory diseases. There are autosomal recessive disorders associated with mutations in genes encoded for SLC46A1 (hereditary folate malabsorption), FOLR1 (cerebral folate deficiency), SLC19A2 (thiamine-responsive megaloblastic anemia), and SLC19A3 (biotin-responsive basal ganglia disease).
还原叶酸载体(RFC,SLC19A1)、硫胺素转运蛋白-1(ThTr1,SLC19A2)和硫胺素转运蛋白-2(ThTr2,SLC19A3)是从同一溶质载体家族进化而来的。SLC19A1 转运叶酸但不转运硫胺素。SLC19A2 和 SLC19A3 转运硫胺素但不转运叶酸。SLC19A1 和 SLC19A2 将其底物输送到全身组织;SLC19A3 介导肠道硫胺素吸收。质子偶联叶酸转运蛋白(PCFT,SLC46A1)是叶酸通过近段小肠顶-刷状缘膜吸收的机制。两种叶酸受体(FOLR1 和 FOLR2)通过内吞过程介导叶酸跨上皮转运。叶酸转运蛋白是治疗癌症和炎症性疾病的药物的输送途径。存在与 SLC46A1(遗传性叶酸吸收不良)、FOLR1(脑叶酸缺乏)、SLC19A2(硫胺素反应性巨幼细胞性贫血)和 SLC19A3(生物素反应性基底节疾病)编码基因的突变相关的常染色体隐性疾病。