为一名患有先天性长QT综合征的儿童在心外膜植入植入式心律转复除颤器。
Epicardially placed implantable cardioverter-defibrillator for a child with congenital long QT syndrome.
作者信息
Sugiyama Hirotaro, Tachibana Motomi, Morita Hiroshi, Nishii Nobuhiro, Miyoshi Akihito, Sugiyama Hiroyasu, Nakagawa Koji, Watanabe Atsuyuki, Nakamura Kazufumi, Ito Hiroshi
机构信息
Department of Cardiology, Okayama University Hospital, 2-5-1 Shikata-cho, Kita-ku, Okayama 700-8558, Japan.
出版信息
J Arrhythm. 2017 Jun;33(3):237-239. doi: 10.1016/j.joa.2016.10.561. Epub 2016 Nov 10.
A 7-year-old boy presented at our hospital with syncope. At birth, electrocardiography had shown a long QT interval with torsade de pointes (TdP). Congenital long QT syndrome (LQTS) had been diagnosed by genetic testing, and was successfully controlled with oral propranolol. At age 7, TdP had recurred with syncope. Electrocardiography revealed a prominent long QT interval with T-wave alternans. The propranolol dose was increased, but TdP remained uncontrolled. A cardioverter-defibrillator (ICD) was implanted epicardially, and TdP completely resolved with atrial pacing. We report this rare case of ICD implantation in a child with LQTS.
一名7岁男孩因晕厥前来我院就诊。出生时，心电图显示QT间期延长并伴有尖端扭转型室速（TdP）。基因检测诊断为先天性长QT综合征（LQTS），口服普萘洛尔后病情得到成功控制。7岁时，TdP再次发作并伴有晕厥。心电图显示QT间期显著延长并伴有T波交替。普萘洛尔剂量增加，但TdP仍未得到控制。遂在心外膜植入心脏复律除颤器（ICD），通过心房起搏后TdP完全消失。我们报告了这例在LQTS患儿中植入ICD的罕见病例。
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