Translational Stem Cell Biology Branch, National Heart, Lung, and Blood Institute, National Institutes of Health, Bethesda, MD 20892, USA.
Translational Stem Cell Biology Branch, National Heart, Lung, and Blood Institute, National Institutes of Health, Bethesda, MD 20892, USA.
Mol Ther. 2021 Nov 3;29(11):3205-3218. doi: 10.1016/j.ymthe.2021.09.001. Epub 2021 Sep 10.
Hematopoietic stem and progenitor cell (HSPC) gene therapies have recently moved beyond gene-addition approaches to encompass targeted genome modification or correction, based on the development of zinc finger nucleases (ZFNs), transcription activator-like effector nucleases (TALENs), and CRISPR-Cas technologies. Advances in ex vivo HSPC manipulation techniques have greatly improved HSPC susceptibility to genetic modification. Targeted gene-editing techniques enable precise modifications at desired genomic sites. Numerous preclinical studies have already demonstrated the therapeutic potential of gene therapies based on targeted editing. However, several significant hurdles related to adverse consequences of gene editing on HSPC function and genomic integrity remain before broad clinical potential can be realized. This review summarizes the status of HSPC gene editing, focusing on efficiency, genomic integrity, and long-term engraftment ability related to available genetic editing platforms and HSPC delivery methods. The response of long-term engrafting HSPCs to nuclease-mediated DNA breaks, with activation of p53, is a significant challenge, as are activation of innate and adaptive immune responses to editing components. Lastly, we propose alternative strategies that can overcome current hurdles to HSPC editing at various stages from cell collection to transplantation to facilitate successful clinical applications.
造血干细胞和祖细胞(HSPC)基因疗法最近已经超越了基因添加方法,涵盖了基于锌指核酸酶(ZFNs)、转录激活因子样效应核酸酶(TALENs)和 CRISPR-Cas 技术的靶向基因组修饰或校正。体外 HSPC 操作技术的进步极大地提高了 HSPC 对基因修饰的敏感性。靶向基因编辑技术可在所需基因组位点进行精确修饰。许多临床前研究已经证明了基于靶向编辑的基因治疗的治疗潜力。然而,在广泛的临床应用之前,仍有几个与基因编辑对 HSPC 功能和基因组完整性的不良后果相关的重大障碍需要克服。本综述总结了 HSPC 基因编辑的现状,重点介绍了现有基因编辑平台和 HSPC 递送方法的效率、基因组完整性和长期植入能力。长期植入的 HSPC 对核酸酶介导的 DNA 断裂的反应,以及 p53 的激活,是一个重大挑战,编辑组件引起的固有和适应性免疫反应的激活也是一个重大挑战。最后,我们提出了替代策略,可以克服从细胞采集到移植各个阶段 HSPC 编辑的当前障碍,从而促进成功的临床应用。