Department of Medicine, Johns Hopkins University, Baltimore, Maryland, USA.
Department of Pediatrics, University of Pittsburgh, Pittsburgh, Pennsylvania, USA.
Pediatr Pulmonol. 2022 Feb;57 Suppl 1(Suppl 1):S89-S100. doi: 10.1002/ppul.25703. Epub 2021 Oct 8.
With improved therapies, people with cystic fibrosis are living longer and healthier lives and increasingly have questions surrounding their sexual and reproductive health. This article will summarize the important issues of which providers should be aware during the lifespan of people with cystic fibrosis, including puberty, adulthood, and menopause. A wide range of sexual and reproductive health topics are addressed such as puberty, transgender and gender nonbinary identities, contraception, sexually transmitted infections, hypogonadism, sexual functioning, cyclical hemoptysis, and urinary incontinence. We discuss gaps in knowledge and current evidence as well as management strategies to optimize care. Our goal is to support providers to enable them to give comprehensive care throughout the lifespan of people with cystic fibrosis.
随着治疗方法的改进,囊性纤维化患者的寿命和生活质量都得到了提高,他们对性健康和生殖健康的问题也越来越关注。本文将总结在囊性纤维化患者的整个生命周期中,包括青春期、成年期和绝经期,医生应该了解的重要问题。本文广泛涉及了性健康和生殖健康的多个主题,如青春期、跨性别和非二元性别认同、避孕、性传播感染、性腺功能减退、性功能、周期性咯血和尿失禁。我们讨论了知识差距和现有证据,以及优化管理策略。我们的目标是支持医疗保健提供者,使他们能够为囊性纤维化患者提供全面的终生护理。