Department of Surgical Pathology, Sapporo Medical University, School of Medicine, Sapporo, Japan.
Department of Respiratory Medicine and Allergology, Sapporo Medical University, School of Medicine, Sapporo, Japan.
Diagn Cytopathol. 2023 May;51(5):E149-E154. doi: 10.1002/dc.25116. Epub 2023 Feb 11.
SMARCA4-deficient undifferentiated tumor (SMARCA4-UT) is a high-grade malignant neoplasm showing undifferentiated or rhabdoid morphology that significantly involves the thorax of adults. It has been reported as SMARCA4-deficient thoracic sarcoma or SMARCA4-deficient non-small cell lung carcinoma according to the findings of immunohistochemical and genetic studies. We report a case of thoracic SMARCA4-UT for which cell block analysis and immunohistochemical staining were useful for the final diagnosis. A 51-year-old man had a chief complaint of left back pain and visited our hospital for further examination. Cytological examination of a left pleural effusion was performed and we also made a cell block of the pleural effusion. Cytological examination revealed polyhedral to round tumor cells. The tumor cells appeared singly or formed loosely cohesive clusters. The nuclei were round to oval, enlarged, and sometimes eccentric with prominent nucleoli with irregular borders. The nuclear chromatin was unevenly distributed. The cytoplasm was vacuolar to eosinophilic. There were no characteristic structures of tumor cells. The cell block revealed many single or loosely cohesive round to epithelioid cells. Some tumor cells often exhibited eccentrically located nuclei and lightly eosinophilic cytoplasm, showing a rhabdoid morphology. On immunohistochemistry, the tumor cells were positive for SOX-2 and they demonstrated significantly reduced SMARCA4 (BRG1) expression; SMARCA2 (BRM) and SMARCB1 (INI1) expression were retained. Accordingly, we made a diagnosis of SMARCA4-UT. This case demonstrates the importance of performing histological and immunohistochemical analysis using cell blocks for immediate diagnosis.
SMARCA4 缺陷未分化肿瘤(SMARCA4-UT)是一种高级别恶性肿瘤,表现为未分化或横纹肌样形态,显著累及成人的胸部。根据免疫组织化学和遗传学研究的结果,它被报道为 SMARCA4 缺陷性胸肉瘤或 SMARCA4 缺陷性非小细胞肺癌。我们报告了一例胸 SMARCA4-UT 病例,细胞块分析和免疫组织化学染色对最终诊断很有用。一名 51 岁男性因左背痛主诉就诊我院进一步检查。对左侧胸腔积液进行细胞学检查,并对胸腔积液进行细胞块制作。细胞学检查显示多面体形至圆形肿瘤细胞。肿瘤细胞呈单个或松散聚集。细胞核呈圆形至椭圆形,增大,有时偏心,核仁突出,边界不规则。核染色质不均匀分布。细胞质呈空泡状至嗜酸性。无肿瘤细胞的特征性结构。细胞块显示许多单个或松散聚集的圆形至上皮样细胞。一些肿瘤细胞常表现为偏心位核和淡嗜酸性细胞质,呈现横纹肌样形态。免疫组织化学染色显示,肿瘤细胞对 SOX-2 呈阳性,并且显著表达 SMARCA4(BRG1)减少;SMARCA2(BRM)和 SMARCB1(INI1)表达保留。因此,我们做出了 SMARCA4-UT 的诊断。该病例表明,使用细胞块进行组织学和免疫组织化学分析对即时诊断很重要。