Hwang Erica, Abdelghaffar Mariam, Shields Bridget E, Damsky William
Department of Dermatology, Yale School of Medicine, New Haven, Connecticut, USA.
School of Medicine, Royal College of Surgeons in Ireland, Busaiteen, Bahrain.
JID Innov. 2023 Aug 10;3(5):100220. doi: 10.1016/j.xjidi.2023.100220. eCollection 2023 Sep.
Inflammatory cutaneous granulomatous diseases, including granuloma annulare, cutaneous sarcoidosis, and necrobiosis lipoidica, are distinct diseases unified by the hallmark of macrophage accumulation and activation in the skin. There are currently no Food and Drug Administration-approved therapies for these conditions except prednisone and repository corticotropin injection for pulmonary sarcoidosis. Treatment of these diseases has generally been guided by low-quality evidence and may involve broadly immunomodulatory medications. Development of new treatments has in part been limited by an incomplete understanding of disease pathogenesis. Recently, there has been substantial progress in better understanding the molecular pathogenesis of these disorders, opening the door for therapeutic innovation. Likewise, reported outcomes of treatment with immunologically targeted therapies may offer insights into disease pathogenesis. In this systematic review, we summarize progress in deciphering the pathomechanisms of these disorders and discuss this in the context of emerging evidence on the use of molecularly targeted therapies in treatment of these diseases.
炎症性皮肤肉芽肿性疾病,包括环状肉芽肿、皮肤结节病和类脂质渐进性坏死,是一类独特的疾病,其共同特征是皮肤中巨噬细胞的积聚和活化。目前,除了用于治疗肺部结节病的泼尼松和促肾上腺皮质激素长效注射剂外,美国食品药品监督管理局尚未批准用于治疗这些疾病的疗法。这些疾病的治疗通常以低质量证据为指导,可能会使用广泛的免疫调节药物。新疗法的开发在一定程度上受到对疾病发病机制理解不完整的限制。最近,在更好地理解这些疾病的分子发病机制方面取得了重大进展,为治疗创新打开了大门。同样,免疫靶向治疗的报告结果可能为疾病发病机制提供见解。在本系统评价中,我们总结了在破译这些疾病发病机制方面取得的进展,并结合有关分子靶向治疗用于治疗这些疾病的新证据进行讨论。