Ribnikar D, Ribeiro J M, Pinto D, Sousa B, Pinto A C, Gomes E, Moser E C, Cardoso M J, Cardoso F
Medical Oncology Department, Institute of Oncology Ljubljana, Ljubljana, Slovenia.
Curr Treat Options Oncol. 2015 Apr;16(4):16. doi: 10.1007/s11864-015-0334-8.
Breast cancer (BC) under age 40 is a complex disease to manage due to the additionally fertility-related factors to be taken in consideration. More than 90% of young patients with BC are symptomatic. Women<40 years are more likely to develop BC with worse clinicopathological features and more aggressive subtype. This has been frequently associated with inferior outcomes. Recently, the prognostic significance of age<40 has been shown to differ according to the BC subtype, being associated with worst recurrence-free survival (RFS) and overall survival (OS) for luminal BC. The biology of BC<40 has also been explored through analysis of large genomic data set, and specific pathways overexpressed in these tumors have been identified which can lead to the development of targeted therapy in the future. A multidisciplinary tumor board should determine the optimal locoregional and systemic management strategies for every individual patient with BC before the start of any therapy including surgery. This applies to both early (early breast cancer (EBC)) and advanced (advanced breast cancer (ABC)) disease, before the start of any therapy. Mastectomy even in young patients confers no overall survival advantage when compared to breast-conserving treatment (BCT), followed by radiotherapy. Regarding axillary approach, indications are identical to other age groups. Young age is one of the most important risk factors for local recurrence after both breast-conserving surgery (BCS) and mastectomy, associated with a higher risk of distant metastasis and death. Radiation after BCS reduces local recurrence from 19.5 to 10.2% in BC patients 40 years and younger. The indications for and the choice of systemic treatment for invasive BC (both early and advanced disease) should not be based on age alone but driven by the biological characteristics of the individual tumor (including hormone receptor status, human epidermal growth factor receptor 2 (HER-2) status, grade, and proliferative activity), disease stage, and patient's comorbidities. Recommendations regarding the use of genomic profiles such as MammaPrint, Oncotype Dx, and Genomic grade index in young women are similar to the general BC population. Especially in the metastatic setting, patient preferences should always be taken into account, as the disease is incurable. The best strategy for these patients is the inclusion into well-designed, independent, prospective randomized clinical trials. Metastatic disease should always be biopsied whenever feasible for histological confirmation and reassessment of biology. Endocrine therapy is the preferred option for hormone receptor-positive disease (HR+ve), even in presence of visceral metastases, unless there is concern or proof of endocrine resistance or there is a need for rapid disease response and/or symptom control. Recommendations for chemotherapy (CT) should not differ from those for older patients with the same characteristics of the metastatic disease and its extent. Young age by itself should not be an indication to prescribe more intensive and combination CT regimens over the sequential use of monotherapy. Poly(ADP-ribose) polymerase inhibitors (PARP inhibitors) represent an important group of promising drugs in managing patients with breast cancer susceptibility gene (BRCA)-1- or BRCA-2-associated BC. Specific age-related side effects of systemic treatment (e.g., menopausal symptoms, change in body image, bone morbidity, cognitive function impairment, fertility damage, sexual dysfunction) and the social impact of diagnosis and treatment (job discrimination, taking care for children) should also be carefully addressed when planning systemic long-lasting therapy, such as endocrine therapy. Survivorship concerns for young women are different compared to older women, including issues of fertility, preservation, and pregnancy.
40岁以下的乳腺癌(BC)是一种复杂的疾病,因为需要考虑额外的生育相关因素。超过90%的年轻乳腺癌患者有症状。40岁以下的女性更有可能患具有更差临床病理特征和更具侵袭性亚型的乳腺癌。这常常与较差的预后相关。最近,已表明40岁以下的预后意义因乳腺癌亚型而异,对于管腔型乳腺癌,与最差的无复发生存期(RFS)和总生存期(OS)相关。也通过对大型基因组数据集的分析探索了40岁以下乳腺癌的生物学特性,并且已确定这些肿瘤中过表达的特定途径,这可能会在未来导致靶向治疗的发展。在包括手术在内的任何治疗开始前,多学科肿瘤委员会应为每位乳腺癌患者确定最佳的局部区域和全身管理策略。这适用于早期(早期乳腺癌(EBC))和晚期(晚期乳腺癌(ABC))疾病,在任何治疗开始前。与保乳治疗(BCT)加放疗相比,即使是年轻患者,乳房切除术也没有总生存优势。关于腋窝处理方法,其适应证与其他年龄组相同。年轻是保乳手术(BCS)和乳房切除术后局部复发的最重要危险因素之一,与远处转移和死亡风险较高相关。40岁及以下乳腺癌患者保乳手术后放疗可将局部复发率从19.5%降至10.2%。浸润性乳腺癌(早期和晚期疾病)全身治疗的适应证和选择不应仅基于年龄,而应由个体肿瘤的生物学特征(包括激素受体状态、人表皮生长因子受体2(HER-2)状态、分级和增殖活性)、疾病分期和患者合并症驱动。关于在年轻女性中使用如MammaPrint、Oncotype Dx和基因组分级指数等基因组谱的建议与一般乳腺癌人群相似。特别是在转移性情况下,应始终考虑患者的偏好,因为该疾病无法治愈。对于这些患者,最佳策略是纳入精心设计、独立、前瞻性随机临床试验。只要可行,转移性疾病应始终进行活检以进行组织学确认和生物学重新评估。内分泌治疗是激素受体阳性疾病(HR+ve)的首选方案,即使存在内脏转移,除非存在内分泌抵抗的担忧或证据,或者需要快速的疾病反应和/或症状控制。对于具有相同转移性疾病特征及其范围的老年患者,化疗(CT)的建议不应有所不同。年轻本身不应成为比序贯使用单药更强化和联合CT方案的指征。聚(ADP-核糖)聚合酶抑制剂(PARP抑制剂)是治疗乳腺癌易感基因(BRCA)-1或BRCA-2相关乳腺癌患者的一类重要的有前景的药物。在规划全身长期治疗(如内分泌治疗)时,还应仔细考虑全身治疗的特定年龄相关副作用(如更年期症状、身体形象改变、骨骼疾病、认知功能损害、生育能力损害、性功能障碍)以及诊断和治疗的社会影响(工作歧视、照顾孩子)。与老年女性相比,年轻女性的生存问题有所不同,包括生育、保留和怀孕问题。